Listening in Spatialized Noise–Sentences (LiSN-S) as a Measure of Auditory Function in Friedreich Ataxia
Shahd Al Haj Ali·David R. Lynch·Jennifer Farmer·Louise Corben·Gary Rance·Sarah Gelbard·Jessica Early
Auditory dysfunction is a clinically significant component of Friedreich ataxia (FRDA), but its features are not readily captured in standard audiology. We examined the Listening in Spatialized Noise–Sentences (LiSN-S) test as a measure of auditory function in a large cohort of subjects with this disease. Methods: We examined 101 individuals with FRDA with the LiSN -S, compared the results with 38 controls, and correlated results with disease features. Results. Control participants scored better